@BEGIN_FILE_ID.DIZ   Description of the Hutchinson-Gilford
progeria syndrome. Source: "Nelson Textbook
   of Pediatrics" by Nelson, Behrman and
   Vaughan; 13th edition, released 1987.
    IS THIS THE ROSWELL "CREATURE" ???
    · ··[ mIC fLAiR/oGN uFO tEAM ]·· ·
@END_FILE_ID.DIZ


Description of the Hutchinson-Gilford progeria syndrome. Source: 
"Nelson Textbook of Pediatrics" by Nelson, Behrman and Vaughan; 13th 
edition, released 1987.

"The Hutchinson-Gilford progeria syndrome has been reported in 86 
patients in the medical literature. The author is also personally 
aware of 16 patients who have not been reported.

[...]

Children with progeria are usually considered to be normal in early 
infancy, but manifestations such as 'scleroderma', midfacial 
cyanosis and 'sculptured nose' may suggest the existence of the 
syndrome at birth. Profound growth failure occurs during the first 
year of life. The characteristic facies, alopecia, loss of 
subcutaneous fat, abnormal posture, stiffness of joints, and bone 
and skin changes become apparent during the second year. Motor and 
mental development are normal.

Features almost   a l w a y s   present when the condition has 
become apparent are short stature; weight distinctly low for height; 
failure to complete sexual maturation; diminished subcutaneous fat; 
head disproportionately large for face; micorgnathia; prominent 
scalp veins; generalized alopecia; prominent eyes; 'plucked-bird 
appearance'; delayed and abnormal dentition; pyriform thorax; short, 
dystrophic clavicles; 'horse-riding' stance; widebased shuffling 
gait; and coxa valga, thin limbs, and prominent, stiff joints. 

Features   f r e q u e n t l y   present are skin that is thin, 
taut, dry, wrinkeled, brown-spotted in various areas, or 
'sclerodermatous' over lower abdomen, proximal thighs, and buttocks; 
prominent superficial veins; loss of eyebrows and eyelashes; 
persistently patent anterior fontanel; 'sculptured', beaked nasal 
tip; faint nasolabial cyanosis; thin lips; protruding ears; absence 
of ear lobes; thin, high-pitched voice; dystrophic nails; and 
progressive radiolucency of terminal phalanges.

[...]

Progeric patients ordinarily develop atherosclerosis and die of 
cardiac or cerebral vascular disease between 7 and 27 year of age, 
with a median age of 13.4 years at death. Many features associated 
with normal aging such as cataracts, presbycusis, presbyopia, arcus 
senilis, ostheoarthritis, or senile personality changes are not 
found. 

No effective treatment for this condition exists."